E75.244 Niemann-Pick disease type A/B

Coding Notes

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Applicable To

Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
Chronic neurovisceral acid sphingomyelinase deficiency

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Code Title
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E75 Disorders of sphingolipid metabolism and other lipid storage disorders
E75.2 Other sphingolipidosis
E75.24 Niemann-Pick disease
E75.244 Niemann-Pick disease type A/B
Applicable to
Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
Chronic neurovisceral acid sphingomyelinase deficiency