I27.0 Primary pulmonary hypertension

Coding Notes

Active
Billable, valid for HIPAA-covered transactions

Type 1 Excludes

persistent pulmonary hypertension of newborn (P29.30)
pulmonary hypertension NOS (I27.20)
secondary pulmonary arterial hypertension (I27.21)
secondary pulmonary hypertension (I27.29)

Applicable To

Heritable pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Primary group 1 pulmonary hypertension
Primary pulmonary arterial hypertension

GEM Conversion to ICD-9 CM


MDC / MS-DRG Reference


Back Reference of Diagnostic Codes

Arrillaga-Ayerza syndrome (pulmonary sclerosis with pulmonary hypertension) I27.0
Arteriosclerosis, arteriosclerotic (diffuse) (obliterans) (of) (senile) (with calcification) I70.90
pulmonary (idiopathic) I27.0
Ayerza's disease or syndrome (pulmonary artery sclerosis with pulmonary hypertension) I27.0
Disease, diseased See also Syndrome
Ayerza's (pulmonary artery sclerosis with pulmonary hypertension) I27.0
heart (organic) I51.9
pulmonary See also Disease, lung
primary (idiopathic) I27.0
Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) I10
primary (idiopathic) I27.0
Sclerosis, sclerotic
pulmonary See Fibrosis, lung
Syndrome See also Disease
Ayerza (-Arrillaga) I27.0
pulmonary

Sibling Codes


Parent Sibling Codes


View in Tabular

Code Title
I00-I99 Diseases of the circulatory system (I00-I99)
I26-I28 Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)
I27 Other pulmonary heart diseases
I27.0 Primary pulmonary hypertension
Type 1 Excludes
persistent pulmonary hypertension of newborn (P29.30)
pulmonary hypertension NOS (I27.20)
secondary pulmonary arterial hypertension (I27.21)
secondary pulmonary hypertension (I27.29)

Applicable to
Heritable pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Primary group 1 pulmonary hypertension
Primary pulmonary arterial hypertension