ICD-10 CM – Browse (Tabular)

Code Title
All Chapters
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D55-D59 Hemolytic anemias (D55-D59)
D56 Thalassemia
D56.0 Alpha thalassemia
Use Additional
code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)

Type 1 Excludes
alpha thalassemia trait or minor (D56.3)
asymptomatic alpha thalassemia (D56.3)
hydrops fetalis due to isoimmunization (P56.0)
hydrops fetalis not due to immune hemolysis (P83.2)

Applicable to
Alpha thalassemia major
Hemoglobin H Constant Spring
Hemoglobin H disease
Hydrops fetalis due to alpha thalassemia
Severe alpha thalassemia
Triple gene defect alpha thalassemia