ICD-10 CM – Browse (Tabular)

Code Title
All Chapters
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E75 Disorders of sphingolipid metabolism and other lipid storage disorders
E75.2 Other sphingolipidosis
E75.24 Niemann-Pick disease
E75.240 Niemann-Pick disease type A
Applicable to
Acid sphingomyelinase deficiency type A (ASMD type A)
Infantile neurovisceral acid sphingomyelinase deficiency