ICD-10 CM – Browse (Tabular)
| Code | Title | 
|---|---|
| – | All Chapters | 
| E00-E89 | Endocrine, nutritional and metabolic diseases (E00-E89) | 
| E70-E88 | Metabolic disorders (E70-E88) | 
| E71 | Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism | 
| E71.3 | 
						Disorders of fatty-acid metabolism
													Type 1 Excludes
						peroxisomal disorders (E71.5)
					 
						Refsum's disease (G60.1)
					 
						Schilder's disease (G37.0)
					 Type 2 Excludes
						carnitine deficiency due to inborn error of metabolism (E71.42)
					  | 
				
| E71.30 | Disorder of fatty-acid metabolism, unspecified | 
| E71.31 | Disorders of fatty-acid oxidation | 
| E71.310 | Long chain/very long chain acyl CoA dehydrogenase deficiency | 
| E71.311 | Medium chain acyl CoA dehydrogenase deficiency | 
| E71.312 | Short chain acyl CoA dehydrogenase deficiency | 
| E71.313 | Glutaric aciduria type II | 
| E71.314 | Muscle carnitine palmitoyltransferase deficiency | 
| E71.318 | Other disorders of fatty-acid oxidation | 
| E71.32 | Disorders of ketone metabolism | 
| E71.39 | Other disorders of fatty-acid metabolism |