E71.3 Disorders of fatty-acid metabolism

Coding Notes

Active
Non-billable / Non-specific, not valid for HIPAA-covered transactions

Type 1 Excludes

peroxisomal disorders (E71.5)
Refsum's disease (G60.1)
Schilder's disease (G37.0)

Tyoe 2 Excludes

carnitine deficiency due to inborn error of metabolism (E71.42)

Child Codes


Sibling Codes


Parent Sibling Codes


View in Tabular

Code Title
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.3 Disorders of fatty-acid metabolism
Type 1 Excludes
peroxisomal disorders (E71.5)
Refsum's disease (G60.1)
Schilder's disease (G37.0)

Type 2 Excludes
carnitine deficiency due to inborn error of metabolism (E71.42)

E71.30 Disorder of fatty-acid metabolism, unspecified
E71.31 Disorders of fatty-acid oxidation
E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
E71.311 Medium chain acyl CoA dehydrogenase deficiency
E71.312 Short chain acyl CoA dehydrogenase deficiency
E71.313 Glutaric aciduria type II
E71.314 Muscle carnitine palmitoyltransferase deficiency
E71.318 Other disorders of fatty-acid oxidation
E71.32 Disorders of ketone metabolism
E71.39 Other disorders of fatty-acid metabolism