E71.5 Peroxisomal disorders

Coding Notes

Active
Non-billable / Non-specific, not valid for HIPAA-covered transactions

Type 1 Excludes

Schilder's disease (G37.0)

Child Codes


Sibling Codes


Parent Sibling Codes


View in Tabular

Code Title
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.5 Peroxisomal disorders
Type 1 Excludes
Schilder's disease (G37.0)

E71.50 Peroxisomal disorder, unspecified
E71.51 Disorders of peroxisome biogenesis
E71.510 Zellweger syndrome
E71.511 Neonatal adrenoleukodystrophy
E71.518 Other disorders of peroxisome biogenesis
E71.52 X-linked adrenoleukodystrophy
E71.520 Childhood cerebral X-linked adrenoleukodystrophy
E71.521 Adolescent X-linked adrenoleukodystrophy
E71.522 Adrenomyeloneuropathy
E71.528 Other X-linked adrenoleukodystrophy
E71.529 X-linked adrenoleukodystrophy, unspecified type
E71.53 Other group 2 peroxisomal disorders
E71.54 Other peroxisomal disorders
E71.540 Rhizomelic chondrodysplasia punctata
E71.541 Zellweger-like syndrome
E71.542 Other group 3 peroxisomal disorders
E71.548 Other peroxisomal disorders