RxDB
ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

E71.4 – Disorders of carnitine metabolism

Overview

Coding Notes

Active
Non-billable / Non-specific, not valid for HIPAA-covered transactions

Type 1 Excludes

Muscle carnitine palmitoyltransferase deficiency (E71.314)

Child Codes

Disorder of carnitine metabolism, unspecified
Primary carnitine deficiency
Carnitine deficiency due to inborn errors of metabolism
Iatrogenic carnitine deficiency
Other secondary carnitine deficiency

Sibling Codes

Maple-syrup-urine disease
Other disorders of branched-chain amino-acid metabolism
Disorder of branched-chain amino-acid metabolism, unspecified
Disorders of fatty-acid metabolism
Peroxisomal disorders

Parent Sibling Codes

Disorders of aromatic amino-acid metabolism
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Other disorders of amino-acid metabolism
Lactose intolerance
Other disorders of carbohydrate metabolism
Disorders of sphingolipid metabolism and other lipid storage disorders
Disorders of glycosaminoglycan metabolism
Disorders of glycoprotein metabolism
Disorders of lipoprotein metabolism and other lipidemias
Disorders of purine and pyrimidine metabolism

View in Tabular

Code Title
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.4 Disorders of carnitine metabolism
Type 1 Excludes
Muscle carnitine palmitoyltransferase deficiency (E71.314)

E71.40 Disorder of carnitine metabolism, unspecified
E71.41 Primary carnitine deficiency
E71.42 Carnitine deficiency due to inborn errors of metabolism
E71.43 Iatrogenic carnitine deficiency
E71.44 Other secondary carnitine deficiency
E71.440 Ruvalcaba-Myhre-Smith syndrome
E71.448 Other secondary carnitine deficiency