ICD-10 CM – Browse (Tabular)

Code Title
All Chapters
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.5 Peroxisomal disorders
E71.51 Disorders of peroxisome biogenesis
Type 1 Excludes
Refsum's disease (G60.1)

Applicable to
Group 1 peroxisomal disorders

E71.510 Zellweger syndrome
E71.511 Neonatal adrenoleukodystrophy
E71.518 Other disorders of peroxisome biogenesis