D66 Hereditary factor VIII deficiency

Coding Notes

Active
Billable, valid for HIPAA-covered transactions

Type 1 Excludes

factor VIII deficiency with vascular defect (D68.0)

Applicable To

Classical hemophilia
Deficiency factor VIII (with functional defect)
Hemophilia NOS
Hemophilia A

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MDC / MS-DRG Reference


Back Reference of Diagnostic Codes

Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute) M19.90
due to or associated with
in (due to)
in (due to)
Deficiency, deficient
anti-hemophilic
factor (A) D66
factor See also Deficiency, coagulation
VIII (congenital) (functional) (hereditary) (with functional defect) D66
Disease, diseased See also Syndrome
Hemophilia (classical) (familial) (hereditary) D66
A D66

Sibling Codes


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Code Title
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D65-D69 Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
D66 Hereditary factor VIII deficiency
Type 1 Excludes
factor VIII deficiency with vascular defect (D68.0)

Applicable to
Classical hemophilia
Deficiency factor VIII (with functional defect)
Hemophilia NOS
Hemophilia A