E72.4 Disorders of ornithine metabolism

Coding Notes

Active
Billable, valid for HIPAA-covered transactions

Type 1 Excludes

hereditary choroidal dystrophy (H31.2-)

Applicable To

Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome
Ornithinemia (types I, II)
Ornithine transcarbamylase deficiency

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Code Title
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E72 Other disorders of amino-acid metabolism
E72.4 Disorders of ornithine metabolism
Type 1 Excludes
hereditary choroidal dystrophy (H31.2-)

Applicable to
Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome
Ornithinemia (types I, II)
Ornithine transcarbamylase deficiency