ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

E74.01 – von Gierke disease

Coding Notes

Active

Billable, valid for HIPAA-covered transactions

Applicable To

Type I glycogen storage disease

GEM Conversion to ICD-9 CM

271.0

Fs: 10000 – Glycogenosis

MDC / MS-DRG Reference

DRG 642

INBORN AND OTHER DISORDERS OF METABOLISM

Back Reference of Diagnostic Codes

Deficiency, deficient

glucose-6-phosphatase E74.01

Disease, diseased See also Syndrome

Gierke's (glycogenosis I) E74.01

glycogen storage E74.00

glucose-6-phosphatase deficiency E74.01

type I E74.01

Von Gierke's E74.01

van Creveld-von Gierke (glycogenosis I) E74.01

von Gierke's (glycogenosis I) E74.01

Gierke's disease (glycogenosis I) E74.01

Van Creveld-von Gierke disease E74.01

Von Gierke's disease E74.01

Sibling Codes

E74.00

Glycogen storage disease, unspecified

E74.02

E74.03

E74.04

McArdle disease

E74.09

Other glycogen storage disease

Parent Sibling Codes

E74.0

Glycogen storage disease

E74.1

Disorders of fructose metabolism

E74.2

Disorders of galactose metabolism

E74.3

Other disorders of intestinal carbohydrate absorption

E74.4

Disorders of pyruvate metabolism and gluconeogenesis

E74.8

Other specified disorders of carbohydrate metabolism

E74.9

Disorder of carbohydrate metabolism, unspecified

View in Tabular

Code	Title
E00-E89	Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88	Metabolic disorders (E70-E88)
E74	Other disorders of carbohydrate metabolism
E74.0	Glycogen storage disease
E74.01	von Gierke disease Applicable to Type I glycogen storage disease