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ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

E75.4 – Neuronal ceroid lipofuscinosis

Overview

Coding Notes

Active
Billable, valid for HIPAA-covered transactions

Applicable To

Batten disease
Bielschowsky-Jansky disease
Kufs disease
Spielmeyer-Vogt disease

GEM Conversion to ICD-9 CM

Fs: 10000 – Cerebral lipidoses

MDC / MS-DRG Reference

DEGENERATIVE NERVOUS SYSTEM DISORDERS WITH MCC
DEGENERATIVE NERVOUS SYSTEM DISORDERS WITHOUT MCC

Back Reference of Diagnostic Codes

Amaurotic idiocy (infantile) (juvenile) (late) E75.4
Batten disease (-Mayou) E75.4
retina E75.4
Bielschowsky disease (-Jansky) E75.4
Ceroid-lipofuscinosis, neuronal E75.4
Degeneration, degenerative
brain (cortical) (progressive) G31.9
in
lipidosis
cerebral E75.4
Disease, diseased See also Syndrome
retina, retinal H35.9
Batten's or Batten-Mayou E75.4
Idiot, idiocy (congenital) F73
amaurotic (Bielschowsky(-Jansky)) (family) (infantile (late)) (juvenile (late)) (Vogt-Spielmeyer) E75.4
Jansky-Bielschowsky amaurotic idiocy E75.4
Kufs' disease E75.4
Lipidosis E75.6
cerebral (infantile) (juvenile) (late) E75.4
cerebroretinal E75.4
Lipofuscinosis, neuronal (with ceroidosis) E75.4
Spielmeyer-Vogt disease E75.4
Vogt-Spielmeyer amaurotic idiocy or disease E75.4

Sibling Codes

GM2 gangliosidosis
Other and unspecified gangliosidosis
Other sphingolipidosis
Sphingolipidosis, unspecified
Other lipid storage disorders
Lipid storage disorder, unspecified

Parent Sibling Codes

Disorders of aromatic amino-acid metabolism
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Other disorders of amino-acid metabolism
Lactose intolerance
Other disorders of carbohydrate metabolism
Disorders of sphingolipid metabolism and other lipid storage disorders
Disorders of glycosaminoglycan metabolism
Disorders of glycoprotein metabolism
Disorders of lipoprotein metabolism and other lipidemias
Disorders of purine and pyrimidine metabolism

View in Tabular

Code Title
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E75 Disorders of sphingolipid metabolism and other lipid storage disorders
E75.4 Neuronal ceroid lipofuscinosis
Applicable to
Batten disease
Bielschowsky-Jansky disease
Kufs disease
Spielmeyer-Vogt disease