ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

E76.22 – Sanfilippo mucopolysaccharidoses

Coding Notes

Active

Billable, valid for HIPAA-covered transactions

Applicable To

Mucopolysaccharidosis, type III (A) (B) (C) (D)

Sanfilippo A syndrome

Sanfilippo B syndrome

Sanfilippo C syndrome

Sanfilippo D syndrome

GEM Conversion to ICD-9 CM

277.5

Fs: 10000 – Mucopolysaccharidosis

MDC / MS-DRG Reference

DRG 642

INBORN AND OTHER DISORDERS OF METABOLISM

Back Reference of Diagnostic Codes

Mucopolysaccharidosis E76.3

Sanfilippo syndrome E76.22

type

III E76.22

Sanfilippo syndrome (Type B) (Type C) (Type D) E76.22

Sibling Codes

E76.21

Morquio mucopolysaccharidoses

E76.29

Other mucopolysaccharidoses

Parent Sibling Codes

E76.0

Mucopolysaccharidosis, type I

E76.1

Mucopolysaccharidosis, type II

E76.2

Other mucopolysaccharidoses

E76.3

Mucopolysaccharidosis, unspecified

E76.8

Other disorders of glucosaminoglycan metabolism

E76.9

Glucosaminoglycan metabolism disorder, unspecified

View in Tabular

Code	Title
E00-E89	Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88	Metabolic disorders (E70-E88)
E76	Disorders of glycosaminoglycan metabolism
E76.2	Other mucopolysaccharidoses
E76.22	Sanfilippo mucopolysaccharidoses Applicable to Mucopolysaccharidosis, type III (A) (B) (C) (D) Sanfilippo A syndrome Sanfilippo B syndrome Sanfilippo C syndrome Sanfilippo D syndrome