ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

E77.0 – Defects in post-translational modification of lysosomal enzymes

Coding Notes

Active

Billable, valid for HIPAA-covered transactions

Applicable To

Mucolipidosis II [I-cell disease]

Mucolipidosis III [pseudo-Hurler polydystrophy]

GEM Conversion to ICD-9 CM

272.7

Fs: 10000 – Lipidoses

MDC / MS-DRG Reference

DRG 642

INBORN AND OTHER DISORDERS OF METABOLISM

Back Reference of Diagnostic Codes

Defect, defective Q89.9

lysosomal enzyme, post-translational modification E77.0

modification, lysosomal enzymes, post-translational E77.0

Disease, diseased See also Syndrome

I-cell E77.0

pseudo-Hurler's E77.0

Mucolipidosis

II, III E77.0

Polydystrophy, pseudo-Hurler E77.0

Pseudo-Hurler's polydystrophy E77.0

Sibling Codes

E77.1

Defects in glycoprotein degradation

E77.8

Other disorders of glycoprotein metabolism

E77.9

Disorder of glycoprotein metabolism, unspecified

Parent Sibling Codes

E70

Disorders of aromatic amino-acid metabolism

E71

Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

E72

Other disorders of amino-acid metabolism

E73

Lactose intolerance

E74

Other disorders of carbohydrate metabolism

E75

Disorders of sphingolipid metabolism and other lipid storage disorders

E76

Disorders of glycosaminoglycan metabolism

E77

Disorders of glycoprotein metabolism

E78

Disorders of lipoprotein metabolism and other lipidemias

E79

Disorders of purine and pyrimidine metabolism

View in Tabular

Code	Title
E00-E89	Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88	Metabolic disorders (E70-E88)
E77	Disorders of glycoprotein metabolism
E77.0	Defects in post-translational modification of lysosomal enzymes Applicable to Mucolipidosis II [I-cell disease] Mucolipidosis III [pseudo-Hurler polydystrophy]