E78.3 Hyperchylomicronemia

Coding Notes

Active
Billable, valid for HIPAA-covered transactions

Applicable To

Chylomicron retention disease
Fredrickson's hyperlipoproteinemia, type I or V
Hyperlipidemia, group D
Mixed hyperglyceridemia

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MDC / MS-DRG Reference


Back Reference of Diagnostic Codes

Chylomicronemia (fasting) (with hyperprebetalipoproteinemia) E78.3
Disease, diseased See also Syndrome
Bürger-Grütz (essential familial hyperlipemia) E78.3
Frederickson's hyperlipoproteinemia, type
hyperlipemic (Bürger-Grütz type) E78.3
Hyperchylomicronemia (familial) (primary) E78.3
Hyperglyceridemia (endogenous) (essential) (familial) (hereditary) (pure) E78.1
group
Fredrickson's type
Lipemia See also Hyperlipidemia
Prebetalipoproteinemia (acquired) (essential) (familial) (hereditary) (primary) (secondary) E78.1
Syndrome See also Disease
Xanthoma (s), xanthomatosis (primary) (familial) (hereditary) E75.5
with
hyperlipoproteinemia

Sibling Codes


Parent Sibling Codes


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Code Title
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E78 Disorders of lipoprotein metabolism and other lipidemias
E78.3 Hyperchylomicronemia
Applicable to
Chylomicron retention disease
Fredrickson's hyperlipoproteinemia, type I or V
Hyperlipidemia, group D
Mixed hyperglyceridemia