ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

E88.49 – Other mitochondrial metabolism disorders

Coding Notes

Active

Billable, valid for HIPAA-covered transactions

GEM Conversion to ICD-9 CM

277.87

Fs: 10000 – Disorders of mitochondrial metabolism

MDC / MS-DRG Reference

DRG 642

INBORN AND OTHER DISORDERS OF METABOLISM

Back Reference of Diagnostic Codes

Disorder (of) See also Disease

metabolism NOS E88.9

mitochondrial E88.40

other specified E88.49

MNGIE syndrome (Mitochondrial Neurogastrointestinal Encephalopathy) E88.49

NARP syndrome (Neuropathy, Ataxia and Retinitis pigmentosa) E88.49

Syndrome See also Disease

Fukuhara E88.49

MNGIE (Mitochondrial Neurogastrointestinal Encephalopathy) E88.49

NARP (Neuropathy, Ataxia and Retinitis pigmentosa) E88.49

Sibling Codes

E88.40

Mitochondrial metabolism disorder, unspecified

E88.41

E88.42

Parent Sibling Codes

E88.0

Disorders of plasma-protein metabolism, not elsewhere classified

E88.1

Lipodystrophy, not elsewhere classified

E88.2

Lipomatosis, not elsewhere classified

E88.3

Tumor lysis syndrome

E88.4

Mitochondrial metabolism disorders

E88.8

Other specified metabolic disorders

E88.9

Metabolic disorder, unspecified

View in Tabular

Code	Title
E00-E89	Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88	Metabolic disorders (E70-E88)
E88	Other and unspecified metabolic disorders
E88.4	Mitochondrial metabolism disorders
E88.49	Other mitochondrial metabolism disorders