J84 Other interstitial pulmonary diseases

Coding Notes

Active
Non-billable / Non-specific, not valid for HIPAA-covered transactions

Type 1 Excludes

drug-induced interstitial lung disorders (J70.2-J70.4)
interstitial emphysema (J98.2)

Tyoe 2 Excludes

lung diseases due to external agents (J60-J70)

Child Codes


Sibling Codes


View in Tabular

Code Title
J00-J99 Diseases of the respiratory system (J00-J99)
J80-J84 Other respiratory diseases principally affecting the interstitium (J80-J84)
J84 Other interstitial pulmonary diseases
Type 1 Excludes
drug-induced interstitial lung disorders (J70.2-J70.4)
interstitial emphysema (J98.2)

Type 2 Excludes
lung diseases due to external agents (J60-J70)

J84.0 Alveolar and parieto-alveolar conditions
J84.01 Alveolar proteinosis
J84.02 Pulmonary alveolar microlithiasis
J84.03 Idiopathic pulmonary hemosiderosis
J84.09 Other alveolar and parieto-alveolar conditions
J84.1 Other interstitial pulmonary diseases with fibrosis
J84.10 Pulmonary fibrosis, unspecified
J84.11 Idiopathic interstitial pneumonia
J84.111 Idiopathic interstitial pneumonia, not otherwise specified
J84.112 Idiopathic pulmonary fibrosis
J84.113 Idiopathic non-specific interstitial pneumonitis
J84.114 Acute interstitial pneumonitis
J84.115 Respiratory bronchiolitis interstitial lung disease
J84.116 Cryptogenic organizing pneumonia
J84.117 Desquamative interstitial pneumonia
J84.17 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
J84.2 Lymphoid interstitial pneumonia
J84.8 Other specified interstitial pulmonary diseases
J84.81 Lymphangioleiomyomatosis
J84.82 Adult pulmonary Langerhans cell histiocytosis
J84.83 Surfactant mutations of the lung
J84.84 Other interstitial lung diseases of childhood
J84.841 Neuroendocrine cell hyperplasia of infancy
J84.842 Pulmonary interstitial glycogenosis
J84.843 Alveolar capillary dysplasia with vein misalignment
J84.848 Other interstitial lung diseases of childhood
J84.89 Other specified interstitial pulmonary diseases
J84.9 Interstitial pulmonary disease, unspecified