ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

M04.1 – Periodic fever syndromes

Coding Notes

Active

Billable, valid for HIPAA-covered transactions

Applicable To

Familial Mediterranean fever

Hyperimmunoglobin D syndrome

Mevalonate kinase deficiency

Tumor necrosis factor receptor associated periodic syndrome [TRAPS]

GEM Conversion to ICD-9 CM

277.31

Fs: 10000 – Familial Mediterranean fever

MDC / MS-DRG Reference

DRG 545

CONNECTIVE TISSUE DISORDERS WITH MCC

DRG 546

CONNECTIVE TISSUE DISORDERS WITH CC

DRG 547

CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC

Back Reference of Diagnostic Codes

Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute) M19.90

in (due to)

Mediterranean fever, familial See also subcategory M14.8- M04.1

Deficiency, deficient

mevalonate kinase M04.1

Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) R50.9

Mediterranean See also Brucellosis A23.9

familial M04.1

periodic (Mediterranean) M04.1

Mediterranean

fever See Brucellosis

familial M04.1

Syndrome See also Disease

hyperimmunoglobulin D M04.1

periodic fever M04.1

tumor necrosis factor receptor associated periodic (TRAPS) M04.1

TRAPS (tumor necrosis factor receptor associated periodic syndrome) M04.1

Sibling Codes

M04.2

Cryopyrin-associated periodic syndromes

M04.8

Other autoinflammatory syndromes

M04.9

Autoinflammatory syndrome, unspecified

Parent Sibling Codes

M00

Pyogenic arthritis

M01

Direct infections of joint in infectious and parasitic diseases classified elsewhere

M02

Postinfective and reactive arthropathies

M04

Autoinflammatory syndromes

M05

Rheumatoid arthritis with rheumatoid factor

M06

Other rheumatoid arthritis

M07

Enteropathic arthropathies

M08

Juvenile arthritis

View in Tabular

Code	Title
M00-M99	Diseases of the musculoskeletal system and connective tissue (M00-M99)
M04-M04	Autoinflammatory syndromes (M04)
M04	Autoinflammatory syndromes
M04.1	Periodic fever syndromes Applicable to Familial Mediterranean fever Hyperimmunoglobin D syndrome Mevalonate kinase deficiency Tumor necrosis factor receptor associated periodic syndrome [TRAPS]