ICD-9-CM Codes ICD-9-PCS Codes

270.3 - Disturbances of branched-chain amino-acid metabolism

GEM Conversion to ICD-10 CM

E71.0

Fs: 10000 – Maple-syrup-urine disease

E71.120

Fs: 10000 – Methylmalonic acidemia

E71.19

Fs: 10000 – Other disorders of branched-chain amino-acid metabolism

E71.2

Fs: 10000 – Disorder of branched-chain amino-acid metabolism, unspecified

Sibling Codes

270.0

Disturbances of amino-acid transport

270.1

Phenylketonuria [PKU]

270.2

Other disturbances of aromatic amino-acid metabolism

270.3

Disturbances of branched-chain amino-acid metabolism

270.4

Disturbances of sulphur-bearing amino-acid metabolism

270.5

Disturbances of histidine metabolism

270.6

Disorders of urea cycle metabolism

270.7

Other disturbances of straight-chain amino-acid metabolism

270.8

Other specified disorders of amino-acid metabolism

270.9

Unspecified disorder of amino-acid metabolism