ICD-10 CM – Browse (Tabular)

Code Title
All Chapters
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89 Certain disorders involving the immune mechanism (D80-D89)
D81 Combined immunodeficiencies
D81.8 Other combined immunodeficiencies
D81.81 Biotin-dependent carboxylase deficiency
Type 1 Excludes
biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

Applicable to
Multiple carboxylase deficiency

D81.810 Biotinidase deficiency
D81.818 Other biotin-dependent carboxylase deficiency
D81.819 Biotin-dependent carboxylase deficiency, unspecified