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ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

D81 – Combined immunodeficiencies

Overview

Coding Notes

Active
Non-billable / Non-specific, not valid for HIPAA-covered transactions

Type 1 Excludes

autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Child Codes

Severe combined immunodeficiency [SCID] with reticular dysgenesis
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
Adenosine deaminase [ADA] deficiency
Nezelof's syndrome
Purine nucleoside phosphorylase [PNP] deficiency
Major histocompatibility complex class I deficiency
Major histocompatibility complex class II deficiency
Other combined immunodeficiencies
Combined immunodeficiency, unspecified

Sibling Codes

Immunodeficiency with predominantly antibody defects
Immunodeficiency associated with other major defects
Common variable immunodeficiency
Other immunodeficiencies
Sarcoidosis
Other disorders involving the immune mechanism, not elsewhere classified

View in Tabular

Code Title
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89 Certain disorders involving the immune mechanism (D80-D89)
D81 Combined immunodeficiencies
Type 1 Excludes
autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3 Adenosine deaminase [ADA] deficiency
D81.30 Adenosine deaminase deficiency, unspecified
D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32 Adenosine deaminase 2 deficiency
D81.39 Other adenosine deaminase deficiency
D81.4 Nezelof's syndrome
D81.5 Purine nucleoside phosphorylase [PNP] deficiency
D81.6 Major histocompatibility complex class I deficiency
D81.7 Major histocompatibility complex class II deficiency
D81.8 Other combined immunodeficiencies
D81.81 Biotin-dependent carboxylase deficiency
D81.810 Biotinidase deficiency
D81.818 Other biotin-dependent carboxylase deficiency
D81.819 Biotin-dependent carboxylase deficiency, unspecified
D81.89 Other combined immunodeficiencies
D81.9 Combined immunodeficiency, unspecified