RxDB
ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

D81.81 – Biotin-dependent carboxylase deficiency

Overview

Coding Notes

Active
Non-billable / Non-specific, not valid for HIPAA-covered transactions

Type 1 Excludes

biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

Applicable To

Multiple carboxylase deficiency

Child Codes

Biotinidase deficiency
Other biotin-dependent carboxylase deficiency
Biotin-dependent carboxylase deficiency, unspecified

Sibling Codes

Other combined immunodeficiencies

Parent Sibling Codes

Severe combined immunodeficiency [SCID] with reticular dysgenesis
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
Adenosine deaminase [ADA] deficiency
Nezelof's syndrome
Purine nucleoside phosphorylase [PNP] deficiency
Major histocompatibility complex class I deficiency
Major histocompatibility complex class II deficiency
Other combined immunodeficiencies
Combined immunodeficiency, unspecified

View in Tabular

Code Title
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89 Certain disorders involving the immune mechanism (D80-D89)
D81 Combined immunodeficiencies
D81.8 Other combined immunodeficiencies
D81.81 Biotin-dependent carboxylase deficiency
Type 1 Excludes
biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

Applicable to
Multiple carboxylase deficiency

D81.810 Biotinidase deficiency
D81.818 Other biotin-dependent carboxylase deficiency
D81.819 Biotin-dependent carboxylase deficiency, unspecified