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ICD-10-CM Codes
Browse (Tabular)
Diagnostic
External
Drug
Neoplasm
D81.3
–
Adenosine deaminase [ADA] deficiency
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Overview
Coding Notes
Removed
Non-billable / Non-specific, not valid for HIPAA-covered transactions
GEM Conversion to ICD-9 CM
277.2
Fs:
10000
–
Other disorders of purine and pyrimidine metabolism
Child Codes
D81.30
Adenosine deaminase deficiency, unspecified
D81.31
Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32
Adenosine deaminase 2 deficiency
D81.39
Other adenosine deaminase deficiency
Sibling Codes
D81.0
Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.4
Nezelof's syndrome
D81.5
Purine nucleoside phosphorylase [PNP] deficiency
D81.6
Major histocompatibility complex class I deficiency
D81.7
Major histocompatibility complex class II deficiency
D81.8
Other combined immunodeficiencies
D81.9
Combined immunodeficiency, unspecified
Parent Sibling Codes
D80
Immunodeficiency with predominantly antibody defects
D81
Combined immunodeficiencies
D82
Immunodeficiency associated with other major defects
D83
Common variable immunodeficiency
D84
Other immunodeficiencies
D86
Sarcoidosis
D89
Other disorders involving the immune mechanism, not elsewhere classified
View in Tabular
Code
Title
D50-D89
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89
Certain disorders involving the immune mechanism (D80-D89)
D81
Combined immunodeficiencies
D81.3
Adenosine deaminase [ADA] deficiency
D81.30
Adenosine deaminase deficiency, unspecified
D81.31
Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32
Adenosine deaminase 2 deficiency
D81.39
Other adenosine deaminase deficiency
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