D68.5 Primary thrombophilia

Coding Notes

Active
Non-billable / Non-specific, not valid for HIPAA-covered transactions

Type 1 Excludes

antiphospholipid syndrome (D68.61)
lupus anticoagulant (D68.62)
secondary activated protein C resistance (D68.69)
secondary antiphospholipid antibody syndrome (D68.69)
secondary lupus anticoagulant with hypercoagulable state (D68.69)
secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)
systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)
thrombotic thrombocytopenic purpura (M31.19)

Applicable To

Primary hypercoagulable states

Child Codes


Sibling Codes


Parent Sibling Codes


View in Tabular

Code Title
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D65-D69 Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
D68 Other coagulation defects
D68.5 Primary thrombophilia
Type 1 Excludes
antiphospholipid syndrome (D68.61)
lupus anticoagulant (D68.62)
secondary activated protein C resistance (D68.69)
secondary antiphospholipid antibody syndrome (D68.69)
secondary lupus anticoagulant with hypercoagulable state (D68.69)
secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)
systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)
thrombotic thrombocytopenic purpura (M31.19)

Applicable to
Primary hypercoagulable states

D68.51 Activated protein C resistance
D68.52 Prothrombin gene mutation
D68.59 Other primary thrombophilia