D89.4 – Mast cell activation syndrome and related disorders
Coding Notes
Active
Non-billable / Non-specific, not valid for HIPAA-covered transactions
Type 1 Excludes
aggressive systemic mastocytosis (C96.21)
congenital cutaneous mastocytosis (Q82.2)
(non-congenital) cutaneous mastocytosis (D47.01)
(indolent) systemic mastocytosis (D47.02)
malignant mast cell neoplasm (C96.2-)
malignant mastocytoma (C96.29)
mast cell leukemia (C94.3-)
mast cell sarcoma (C96.22)
mastocytoma NOS (D47.09)
other mast cell neoplasms of uncertain behavior (D47.09)
systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)
Child Codes
Sibling Codes
Parent Sibling Codes
View in Tabular
| Code | Title |
|---|---|
| D50-D89 | Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) |
| D80-D89 | Certain disorders involving the immune mechanism (D80-D89) |
| D89 | Other disorders involving the immune mechanism, not elsewhere classified |
| D89.4 |
Mast cell activation syndrome and related disorders
Type 1 Excludes
aggressive systemic mastocytosis (C96.21)
congenital cutaneous mastocytosis (Q82.2)
(non-congenital) cutaneous mastocytosis (D47.01)
(indolent) systemic mastocytosis (D47.02)
malignant mast cell neoplasm (C96.2-)
malignant mastocytoma (C96.29)
mast cell leukemia (C94.3-)
mast cell sarcoma (C96.22)
mastocytoma NOS (D47.09)
other mast cell neoplasms of uncertain behavior (D47.09)
systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)
|
| D89.40 | Mast cell activation, unspecified |
| D89.41 | Monoclonal mast cell activation syndrome |
| D89.42 | Idiopathic mast cell activation syndrome |
| D89.43 | Secondary mast cell activation |
| D89.44 | Hereditary alpha tryptasemia |
| D89.49 | Other mast cell activation disorder |