E75.241 Niemann-Pick disease type B

Coding Notes

Active
Billable, valid for HIPAA-covered transactions

Applicable To

Acid sphingomyelinase deficiency type B (ASMD type B)
Chronic visceral acid sphingomyelinase deficiency

GEM Conversion to ICD-9 CM

Fs: 10000 Lipidoses

MDC / MS-DRG Reference


Back Reference of Diagnostic Codes


Sibling Codes


Parent Sibling Codes


Codes with Same Suffix


View in Tabular

Code Title
E00-E89 Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 Metabolic disorders (E70-E88)
E75 Disorders of sphingolipid metabolism and other lipid storage disorders
E75.2 Other sphingolipidosis
E75.24 Niemann-Pick disease
E75.241 Niemann-Pick disease type B
Applicable to
Acid sphingomyelinase deficiency type B (ASMD type B)
Chronic visceral acid sphingomyelinase deficiency